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J Hand Microsurg 2018; 10(02): 109-112
DOI: 10.1055/s-0038-1626682
Case Report
Thieme Medical and Scientific Publishers Private Ltd.

Lipofibromatous Hamartoma of the Palmar Cutaneous Branch of the Median Nerve

Jason S. Hoellwarth
1   Department of Orthopaedic Surgery, University of Pittsburgh Medical Center, Pittsburgh, Pennsylvania, United States
,
Robert J. Goitz
1   Department of Orthopaedic Surgery, University of Pittsburgh Medical Center, Pittsburgh, Pennsylvania, United States
› Author Affiliations Funding None.
Further Information

Publication History

Received: 06 August 2017

Accepted: 21 December 2017

Publication Date:
03 April 2018 (online)

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Abstract

Background Lipofibromatous hamartoma (LFH) is a benign tumor of peripheral nerves, most commonly reported in the median nerve, and often associated with carpal tunnel symptoms. There have been nearly 200 reported cases of LFH in the median nerve, but to the authors’ knowledge, this 10-year-old girl represents the first case report involving the palmar cutaneous branch.

Methods An excisional biopsy of the mass was performed via a standard midline palmar incision. The tumor was found encapsulating the palmar cutaneous branch, and thus it was sacrificed.

Results The incision healed without issue, but the patient reported numbness in the palm of her hand as was expected.

Conclusion LFH is a benign tumor, although it can cause symptoms due to mass effect. If the diagnosis is uncertain or a patient is symptomatic, excisional biopsy can be performed even if involving a cutaneous nerve.

Keywords

lipofibromatous hamartoma - hamartoma - palmar cutaneous branch - median nerve - median nerve tumor
 

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