Diagnostikalgorithmus der pulmonalen Hypertonie

Elena Pfeuffer-Jovic; Kai Helge Schmidt; Teresa John; Tilmann Kramer; Agata Makowska; Julian Müller; Heinrike Wilkens; Matthias Held

doi:10.1055/a-2625-4814

Pneumologie, Inhaltsverzeichnis

Pneumologie 2025; 79(10): 732-740
DOI: 10.1055/a-2625-4814

Übersicht

Diagnostikalgorithmus der pulmonalen Hypertonie

Diagnostic Algorithm for Pulmonary Hypertension

Authors

Elena Pfeuffer-Jovic

¹Medizinische Klinik mit Schwerpunkt Pneumologie und Beatmungsmedizin, Klinikum Würzburg Mitte gGmbH, Würzburg, Deutschland
Kai Helge Schmidt

²Zentrum für Kardiologie, Kardiologie I, Universitätsmedizin Mainz, Mainz, Deutschland

³Centrum für Thrombose und Hämostase (CTH), Universitätsmedizin Mainz, Mainz, Deutschland
Teresa John

⁴Klinische Abteilung für Pneumologie, Universitätsklinik für Innere Medizin, Universitätsklinikum Graz, Graz, Österreich
Tilmann Kramer

⁵Klinik III für Innere Medizin, Herzzentrum der Uniklinik Köln, Köln, Deutschland
Agata Makowska

⁶Zentrum für Pulmonale Hypertonie, Thoraxklinik Heidelberg gGmbH am Universitätsklinikum Heidelberg, Heidelberg, Deutschland
Julian Müller

⁷Klinik für Pneumologie, Universitätsklinikum Zürich, Zürich, Schweiz
Heinrike Wilkens

⁸Klinik für Innere Medizin 5, Universitätsklinikum des Saarlandes, Homburg/Saar, Deutschland
Matthias Held

¹Medizinische Klinik mit Schwerpunkt Pneumologie und Beatmungsmedizin, Klinikum Würzburg Mitte gGmbH, Würzburg, Deutschland

Abstract

Zusammenfassung

Für die Diagnose der pulmonalen Hypertonie (PH) wird ein schrittweiser diagnostischer Algorithmus empfohlen, um die Patient*innen, die an ein PH-Zentrum überwiesen werden müssen und eine invasive hämodynamische Bewertung benötigen, zu identifizieren. Bei hoher Wahrscheinlichkeit für eine pulmonalarterielle Hypertonie oder chronisch thromboembolische PH wird eine schnelle Überweisung an ein PH-Zentrum zu jedem Zeitpunkt während der diagnostischen Abklärung empfohlen. Auch Patienten mit interstitieller Lungenerkrankung und Verdacht auf PH sowie Patienten mit pulmonalen Erkrankungen oder Erkrankungen des linken Herzens und Verdacht auf schwere PH sollten an ein PH-Expertenzentrum überwiesen werden.

Abstract

For the diagnosis of pulmonary hypertension (PH), a stepwise diagnostic algorithm is recommended to identify patients who require referral to a PH center and who require invasive hemodynamic assessment. In cases of high probability of pulmonary arterial hypertension or chronic thrombo-embolic PH, prompt referral to a PH center is recommended at any time during the diagnostic workup. Patients with interstitial lung disease and suspected PH, as well as patients with pulmonary disease or left heart disease and suspected severe PH, should also be referred to a PH expert center.

Schlüsselwörter

pulmonale Hypertonie - Echokardiografie - Diagnostik - Rechtsherzkatheter

Keywords

pulmonary hypertension - echocardiography - diagnostics - right heart catherization

Volltext

Referenzen

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