Bicameral Repair of Right Pulmonary Artery to Left Atrial Communication

Abstract

A right pulmonary artery to left atrial communication is a very rare vascular congenital anomaly. Patients most commonly present in the neonatal period with congestive cardiac failure or at a later stage with central cyanosis and its complications. Various diagnostic modalities are available but angiography is the most important decision-making tool for the management of this lesion. We present an unusual case of right pulmonary artery to left atrial communication in a 14-year-old patient, who underwent successful surgical repair through a bicameral approach.

Keywords

congenital heart disease - aneurysm - pulmonary arteries/veins - arteriovenous fistula - cyanosis

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