Common Iliac Artery Aneurysm and Spontaneous Dissection with Contralateral Iatrogenic Common Iliac Artery Dissection in Classic Ehlers–Danlos Syndrome

Sachin Mehta; Shweta U. Dhar; Yochai Birnbaum

doi:10.1055/s-0032-1325118

International Journal of Angiology, Table of Contents

Int J Angiol 2012; 21(03): 167-170
DOI: 10.1055/s-0032-1325118

Case Report

Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Common Iliac Artery Aneurysm and Spontaneous Dissection with Contralateral Iatrogenic Common Iliac Artery Dissection in Classic Ehlers–Danlos Syndrome

Sachin Mehta

¹Division of Cardiology, Department of Medicine, Baylor College of Medicine, Houston, Texas

,

Shweta U. Dhar

²Department of Molecular and Human Genetics, Baylor College of Medicine, Houston, Texas

,

Yochai Birnbaum

¹Division of Cardiology, Department of Medicine, Baylor College of Medicine, Houston, Texas

› Author Affiliations

Abstract

We describe a 43-year-old man who developed a spontaneous dissection of a right iliac artery aneurysm after performing vigorous physical exercise. Additionally, during peripheral intervention, the patient developed iatrogenic dissection of the left iliac artery. The patient had the characteristic physical findings of Ehlers–Danlos syndrome (EDS), classic type. Genetic testing revealed a mutation in the COL5A1 gene associated with EDS, classic type. Vascular aneurysms and dissections are characteristics of EDS vascular type, but not the classic type. Only one previous case with EDS, classic type with spontaneous iliac artery dissection has been described.

Keywords

Ehlers–Danlos syndrome - iliac artery aneurysm - spontaneous arterial dissection

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References

References
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