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J Neurol Surg Rep 2013; 74(02): 105-110
DOI: 10.1055/s-0033-1351115
Georg Thieme Verlag KG Stuttgart · New York

Fibromyxoma of the Lateral Skull Base in a Child: Case Report

Paul Klimo Jr.
1   Murphey Neurologic & Spine Institute, Semmes, Memphis, Tennessee, United States
2   Le Bonheur Children's Hospital, Memphis, Tennessee, United States
3   Department of Neurosurgery, University of Tennessee Health Science Center, Memphis, Tennessee, United States
4   St. Jude Children's Research Hospital, Memphis, Tennessee, United States
,
Tushar Jha
5   Department of Neurosurgery, Georgetown University, Washington, District of Columbia, United States
,
Asim F. Choudhri
2   Le Bonheur Children's Hospital, Memphis, Tennessee, United States
3   Department of Neurosurgery, University of Tennessee Health Science Center, Memphis, Tennessee, United States
6   Department of Radiology, University of Tennessee Health Science Center, Memphis, Tennessee, United States
,
Royce Joyner
2   Le Bonheur Children's Hospital, Memphis, Tennessee, United States
7   Department of Pathology, University of Tennessee Health Science Center, Memphis, Tennessee, United States
,
L. Madison Michael II
1   Murphey Neurologic & Spine Institute, Semmes, Memphis, Tennessee, United States
3   Department of Neurosurgery, University of Tennessee Health Science Center, Memphis, Tennessee, United States
› Author Affiliations
Further Information

Publication History

15 January 2013

14 June 2013

Publication Date:
30 July 2013 (online)

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Abstract

Purpose Fibromyxomas and myxomas are benign tumors of mesenchymal origin usually found outside the nervous system, most commonly in the atrium of the heart. They can also arise in the mandible or maxilla, but it is exceedingly rare to find them within the skull base. The history, histologic features, and the literature, with emphasis on other pediatric cases, are reviewed for this uncommon skull base neoplasm.

Methods We describe the case of a 13-year-old girl who presented with a 1-year history of facial weakness, numbness, and hearing loss. A large locally destructive tumor centered in the petrous bone was found on magnetic resonance imaging.

Results A mastoidectomy combined with a middle fossa craniotomy was performed for gross total resection. The child is disease free 12 months after surgery.

Conclusion Diagnosis could not be made solely on radiographic studies because of the lack of pathognomonic imaging features. Radical resection provided the patient the best chance of cure. Long-term surveillance is necessary to monitor for tumor recurrence.

Keywords

fibromyxoma - myxoma - child - pediatric - skull base - petrous - mesenchymal - tumor - benign
 

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