Foix-Alajouanine Syndrome Presenting as Acute Cauda Equina Syndrome: A Case Report
21 November 2013
17 March 2014
22 May 2014 (eFirst)
Study Design Case report.
Objective Present a case of Foix-Alajouanine syndrome that presented as acute cauda equina syndrome and discuss the pathophysiology and management.
Methods An adult male patient developed sudden onset of back pain and leg pain with weakness of the lower limbs and bladder/bowel dysfunction typical of cauda equina syndrome. Emergency magnetic resonance imaging revealed no compressive lesion in the spine but showed tortuous flow voids and end-on blood vessels in the peridural region suggesting spinal arteriovenous malformation resulting in Foix-Alajouanine syndrome.
Results The case was managed by endovascular embolization with excellent results. The pathophysiology, imaging features, management, and literature review of the syndrome is discussed.
Conclusion The authors conclude that this condition may be an important differential diagnosis for cauda equina syndrome.
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