Reconstruction of the Large Face and Scalp Defects of a Patient with Sturge–Weber Syndrome
01 June 2016 (online)
Sturge–Weber syndrome (SWS) is named after British physicians William A. Sturge, who first described the condition, and Frederick Parkes Weber, who first demonstrated its linkage with intracranial calcifications. SWS affects 1 in every 20,000 to 50,000 live births worldwide and is associated with facial and cerebral vascular malformations. It has been reported that 3% of patients with a facial port wine stain were diagnosed with SWS. This rare syndrome can also present with seizures as a result of intracranial vascular malformation, as well as visual disturbances secondary to retinal detachment. When SWS hemangiomas are localized in the head and neck region, these patients are often managed by dermatologic and plastic surgeons due to the functional and cosmetic residues of these lesions.