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Facial Plast Surg 2016; 32(02): 133-141
DOI: 10.1055/s-0036-1582231
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Congenital Anomalies of the Nose

Jamie L. Funamura
1   Department of Otolaryngology and Communication Enhancement, Children's Hospital Boston, Boston, Massachusetts
,
Travis T. Tollefson
2   Department of Otolaryngology, University of California, Davis, Sacramento, California
› Author Affiliations
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Publication History

Publication Date:
20 April 2016 (online)

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Abstract

Congenital anomalies of the nose range from complete aplasia of the nose to duplications and nasal masses. Nasal development is the result of a complex embryologic patterning and fusion of multiple primordial structures. Loss of signaling proteins or failure of migration or proliferation can result in structural anomalies with significant cosmetic and functional consequences. Congenital anomalies of the nose can be categorized into four broad categories: (1) aplastic or hypoplastic, (2) hyperplastic or duplications, (3) clefts, and (4) nasal masses. Our knowledge of the embryologic origin of these anomalies helps dictate subsequent work-up for associated conditions, and the appropriate treatment or surgical approach to manage newborns and children with these anomalies.

Keywords

nasal deformities - nasal dermoid - Tessier cleft - nasal cleft - nasal hemangioma
 

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