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Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery 2016; 35(03): 234-238
DOI: 10.1055/s-0036-1584552
Case Report | Relato de Caso
Thieme Publicações Ltda Rio de Janeiro, Brazil

Extra-Axial Cerebello-Pontine Angle Medulloblastoma

Meduloblastoma extra-axial no ângulo ponto-cerebelar
Rodrigo Moreira Faleiro
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
,
Vítor Vieira de Souza Moraes
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
,
Maria Teresa de Seixas Alves
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
,
Moises Salgado Pedrosa
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
,
Luiz Alberto Otoni Garcia
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
,
Renato Rinco Fontoura
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
,
Vanessa Alves Lobato
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
,
Diego Silveira Rodrigues
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
,
Laura Vilaça Carvalho Viégas Martins
1   Department of Neurosurgery, Hospital Felício Rocho, Belo Horizonte, MG, Brazil
› Author Affiliations
Further Information

Publication History

16 August 2015

08 April 2016

Publication Date:
14 June 2016 (online)

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Abstract

Medulloblastoma is the most common central nervous system tumor in children. Extra-axial medulloblastomas, especially tumors with no connection to the brain stem or cerebellum are extremely rare. We report a case of a 3-year-old patient, who presented with a history of subacute headache and vomiting. After performing a head computed tomography scan, a mass was detected in the left cerebello-pontine angle, along with concomitant hydrocephalus. The treatment was total resection of the tumor. Despite the fact that extra-axial medulloblastomas are extremely rare, this differential diagnosis should be included in the management of pediatric patients who present with posterior fossa tumors.

Resumo

Meduloblastoma é o tumor do sistema nervoso central mais comum em crianças. Meduloblastomas extra-axiais, especialmente tumores sem conexão com o tronco encefálico ou cerebelo, são extremamente raros. Relatamos o caso de uma paciente de 3 anos de idade, que apresentou um histórico de cefaleia subaguda e vômitos. Por meio de um exame de tomografia computadorizada, foi identificada uma massa no ângulo ponto-cerebelar esquerdo, acompanhada de hidrocefalia. O tratamento foi resseção total do tumor. Apesar de meduloblastomas extra-axiais serem extremamente raros, este diagnóstico diferencial deve ser incluído no manejo de pacientes pediátricos que apresentem tumores da fossa posterior.

Keywords

medulloblastoma - cerebellum - pediatric - children - tumor - neurosurgery

Palavras-chave

meduloblastoma - cerebelo - pediatria - crianças - tumor - neurocirurgia
 

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