CC-BY-NC-ND 4.0 · THORAC CARDIOV SURG Reports 2017; 06(01): e10-e14
DOI: 10.1055/s-0037-1598625
Case Report: Thoracic
Georg Thieme Verlag KG Stuttgart · New York

It's Rare So Be Aware: Pleuropulmonary Blastoma Mimicking Congenital Pulmonary Airway Malformation

Fayza Haider1, Khulood Al Saad2, Fatima Al-Hashimi3, Hakima Al-Hashimi4
  • 1Pediatric Surgery Unit, Department of Surgery, Salmaniya Medical Complex, Manama, Bahrain
  • 2Pediatric Department, Salmaniya Medical Complex, Manama, Bahrain
  • 3Department of Pathology, Salmaniya Medical Complex, Manama, Bahrain
  • 4Department of Radiology, Salmaniya Medical Complex, Manama, Bahrain
Further Information

Publication History

30 October 2016

10 January 2017

Publication Date:
11 April 2017 (online)

Abstract

Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood. The tumor arises in the lung and pleura and is regarded as a pulmonary dysontogenetic or embryonic neoplasm. Four types are defined in literature. Type I PPB is a rare, cystic lung neoplasm in infants characterized by subtle malignant changes and a good prognosis. Recurrences after type I PPB are usually advanced with a poor prognosis.

We report this case to increase awareness about this entity so that the pediatricians, pediatric surgeons, radiologist, and pathologist recognize it early.