CC-BY-NC-ND 4.0 · THORAC CARDIOV SURG Reports 2017; 06(01): e10-e14
DOI: 10.1055/s-0037-1598625
Case Report: Thoracic
Georg Thieme Verlag KG Stuttgart · New York

It's Rare So Be Aware: Pleuropulmonary Blastoma Mimicking Congenital Pulmonary Airway Malformation

Fayza Haider
Pediatric Surgery Unit, Department of Surgery, Salmaniya Medical Complex, Manama, Bahrain
Khulood Al Saad
Pediatric Department, Salmaniya Medical Complex, Manama, Bahrain
Fatima Al-Hashimi
Department of Pathology, Salmaniya Medical Complex, Manama, Bahrain
Hakima Al-Hashimi
Department of Radiology, Salmaniya Medical Complex, Manama, Bahrain
› Author Affiliations
Further Information

Publication History

30 October 2016

10 January 2017

Publication Date:
11 April 2017 (online)


Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood. The tumor arises in the lung and pleura and is regarded as a pulmonary dysontogenetic or embryonic neoplasm. Four types are defined in literature. Type I PPB is a rare, cystic lung neoplasm in infants characterized by subtle malignant changes and a good prognosis. Recurrences after type I PPB are usually advanced with a poor prognosis.

We report this case to increase awareness about this entity so that the pediatricians, pediatric surgeons, radiologist, and pathologist recognize it early.