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DOI: 10.1055/s-0039-1686332
Mastoidal manifestation of histiocytosis in a young woman
Introduction:
Histiocytosis is a rare systemic disease. It is defined as an inflammatory myeloid neoplasm. Isolated pulmonary manifestations are most common in adults.
We present a young woman with an extended manifestation in the mastoid.
Case
The Patient presented initially otalgia and otorrhea. Examination showed an inflammation of the outer ear canal. The patient was diagnosed with pulmonary histiocytosis two years ago, but no therapy was required at that time. A diabetes insipidus was also known.
A few days later she returned with vertigo. The CT scan revealed an extendend osteolytic process of the mastoid. A mastoidectomy was performed. Histology showed a manifestation of histiocytosis.
Therapy
Chemotherapy with cytarabine was started. So far, the patient showed no complications.
Conclusion:
Histiocytosis is a rare disease. Pulmonary and osseous manifestations are most common.
In our case, pulmonary manifestations in combination with diabetes insipidus as a first sign of a manifestation of the central nervous system led early to the diagnosis of a manifestation of the mastoid.
Publication History
Publication Date:
23 April 2019 (online)
© 2019. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).
Georg Thieme Verlag KG
Stuttgart · New York