CC BY-NC-ND 4.0 · AJP Rep 2019; 09(04): e357-e360
DOI: 10.1055/s-0039-3400317
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Postnatal Amelioration of Fetal Right Ventricular Hypoplasia Associated with Large Eustachian Valve: A Case Report

Ayaka Iwatani
1   Department of Pediatrics, Saitama Medical Center, Saitama Medical University, Saitama, Japan
,
Fumihito Miyake
1   Department of Pediatrics, Saitama Medical Center, Saitama Medical University, Saitama, Japan
,
Hirotaka Ishido
1   Department of Pediatrics, Saitama Medical Center, Saitama Medical University, Saitama, Japan
,
Masayo Kanai
1   Department of Pediatrics, Saitama Medical Center, Saitama Medical University, Saitama, Japan
,
Akio Ishiguro
1   Department of Pediatrics, Saitama Medical Center, Saitama Medical University, Saitama, Japan
,
Yoichi Iwamoto
1   Department of Pediatrics, Saitama Medical Center, Saitama Medical University, Saitama, Japan
,
Kazuhiko Kabe
1   Department of Pediatrics, Saitama Medical Center, Saitama Medical University, Saitama, Japan
,
Satoshi Masutani
1   Department of Pediatrics, Saitama Medical Center, Saitama Medical University, Saitama, Japan
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Weitere Informationen

Publikationsverlauf

07. November 2018

11. Januar 2019

Publikationsdatum:
19. November 2019 (online)

Abstract

In fetuses, the Eustachian valve directs oxygenated blood returning from the inferior vena cava into the left atrium via the foramen ovale. If too large, the Eustachian valve can restrict right ventricular inflow, as well as induce postnatal cyanosis via an interatrial right-to-left shunt. We report a fetal case of postnatal amelioration of the tricuspid valve and right ventricle hypoplasia, despite significant right ventricular hypoplasia associated with a large Eustachian valve. Application of an appropriate respiratory management regimen to help reduce pulmonary vascular resistance is of particular importance for the reversal of the right-to-left shunt via the foramen ovale and associated increases in right ventricular inflow.

 
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