Image of the Month: Decision-Making in Surgery for Late Onset Hirschsprung Disease

Anisha Apte; Elise McKenna; Marc A. Levitt

doi:10.1055/s-0040-1721049

European Journal of Pediatric Surgery Reports, Inhaltsverzeichnis

CC BY 4.0 · European J Pediatr Surg Rep. 2020; 08(01): e99-e101
DOI: 10.1055/s-0040-1721049

Case Report

Image of the Month: Decision-Making in Surgery for Late Onset Hirschsprung Disease

Authors

Anisha Apte

¹Department of Surgery, The George Washington University School of Medicine and Health Sciences, Washington, District of Columbia, United States
Elise McKenna

²Department of General and Thoracic Surgery, Children's National Medical Center, Washington, District of Columbia, United States
Marc A. Levitt

¹Department of Surgery, The George Washington University School of Medicine and Health Sciences, Washington, District of Columbia, United States

²Department of General and Thoracic Surgery, Children's National Medical Center, Washington, District of Columbia, United States

³Division of Colorectal and Pelvic Reconstruction Surgery, Children's National Medical Center, Washington, District of Columbia, United States

Abstract

We present a case of a 14-year-old boy with chronic distension, poor growth, and chronic constipation. He undergoes anorectal manometry and rectal biopsy, confirming the diagnosis of Hirschsprung disease (HD). The case is presented with a key image and associated questions to prompt discussion on strategies for management and treatment of HD in late-diagnosed children.

Keywords

Hirschsprung disease - chronic distension - colonic dysmotility - chronic constipation - pull-through

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Referenzen

References
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