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CC BY 4.0 · European J Pediatr Surg Rep. 2021; 09(01): e28-e32
DOI: 10.1055/s-0041-1726347
Case Report

Skip Segment Hirschsprung Disease Managed by Pull-Through of the Right Colon

Hira Ahmad
1   Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital Columbus, Ohio, United States
,
Alejandra Vilanova-Sánchez
2   Colorectal and Urogenital Reconstruction Unit, La Paz University Hospital, Madrid, Spain
,
Isabel Amengual
3   Department of Pathology, Son Espases University Hospital, Palma de Mallorca, Illes Balears, Spain
,
Laura Guerra-Pastrian 
4   Department of Pathology, La Paz University Hospital, Madrid, Madrid, Spain
,
Marta Garrido-Pontnou
5   Department of Pathology, Vall d'Hebron Hospital Universitari, Barcelona, Catalunya, Spain
,
Cristina Montalvo
6   Department of Pediatric Surgery, Son Espases University Hospital, Palma de Mallorca, Illes Balears, Spain
,
Alba Bueno
7   Department of Pediatric Surgery, Hospital Universitario La Paz, Paseo de la Castellana 261, Madrid, Madrid, Spain
,
Jacob Langer
1   Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital Columbus, Ohio, United States
8   Division of General and Thoracic Surgery, SickKids, Toronto, Ontario, Canada
,
Richard J. Wood
1   Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital Columbus, Ohio, United States
,
Marc A. Levitt
9   Division of Colorectal and Pelvic Reconstructive Surgery, Children's National Medical Center, Washington, District of Columbia, United States
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Abstract

Hirschsprung disease is the most common neurocristopathy in children, resulting in the congenital loss of enteric ganglia. Rare reports of skip lesions have previously been reported in the literature. We present a case of skip lesions known prior to surgery and managed by pull-through of the right colon that allowed the preservation of the colon.

Keywords

calretinin stain - reoperation - enterocolitis - continence - aganglionosis


Publication History

Received: 14 August 2020

Accepted: 18 January 2021

Article published online:
25 March 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

Georg Thieme Verlag KG
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