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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2021; 31(01): 203-209
DOI: 10.1055/s-0041-1729770
Pictorial Essay

Extraosseous Ewing’s Sarcoma: Pictorial Review of Imaging Findings, Differential Diagnosis, and Pathologic Correlation

Alan Alexander
1   Department of Radiolog, Imaging Medical Associates, Inc., Northridge, California, United States
,
Kyle Hunter
2   Department of Radiology, Cleveland Clinic, Cleveland, Ohio, United States
,
Michael Rubin
3   Department of Radiology, Akron Children’s Hospital, Akron, Ohio, United States
,
Ambarish P. Bhat
4   Section of Vascular and Interventional Radiology, Department of Radiology, University of Missouri Columbia, Columbia, Missouri, United States
› Author Affiliations Funding None.
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Abstract

Extraosseous Ewing’s sarcoma (EES), first described in 1969, is a malignant mesenchymal tumor just like its intraosseous counterpart. Although Ewing’s sarcomas are common bone tumors in young children, EESs are rarer and more commonly found in older children/adults, often carrying a poorer prognosis. We discuss the multimodality imaging features of EES and the differential diagnosis of an aggressive appearing mass in proximity to skeletal structures, with pathologic correlates. This review highlights the need to recognize the variability of radiologic findings in EES such as the presence of hemorrhage, rich vascularity, and cystic or necrotic regions and its imaging similarity to other neoplasms that are closely related pathologically.

Keywords

Ewing’s sarcoma - musculoskeletal soft tissue - oncology - pediatric - rhabdomyosarcoma


Publication History

Article published online:
31 May 2021

© 2021. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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