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Int J Angiol 2023; 32(04): 292-295
DOI: 10.1055/s-0041-1729921
Case Report

Klippel–Trénaunay Syndrome and Developmental Coxa Vara in the Same Limb: A Case Report with a Review of the Literature

Balaji Zacharia 
1   Department Of Orthopedics, Government Medical College, Kozhikode, Kerala, India
,
Jittu Alex
1   Department Of Orthopedics, Government Medical College, Kozhikode, Kerala, India
,
Ashwin Rajmohan
1   Department Of Orthopedics, Government Medical College, Kozhikode, Kerala, India
› Author Affiliations Funding We have not accepted any financial assistance from within or outside our institution for collecting data, writing the manuscript, or for its publications.
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Abstract

We present a case of a 14-year-old girl who was first treated when she was 4 years old. She had progressive limping of the left lower limb from the age of 3 years. She was diagnosed to have developmental coxa vara of the left hip and treated by a subtrochanteric valgus osteotomy of the left femur. Later, she developed hypertrophy of the left upper and lower limbs. There were port-wine stains over the left lower limbs with multiple superficial varicosities. Her diagnosis was Klippel–Trénaunay syndrome (KTS). She is asymptomatic at the final follow-up. Both developmental coxa vara and KTS are rare conditions. We present this case to demonstrate the rarest combination of two rare conditions occurring in the same limb.

Keywords

Klippel–Trénaunay syndrome - developmental coxa vara - hypertrophy of limb - port-wine stain


Publication History

Article published online:
30 July 2021

© 2021. International College of Angiology. This article is published by Thieme.

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