A Case Series of Budd–Chiari Syndrome in Nigerian Patients: Diagnosis, Associations, Management, and Outcomes

Abstract

Budd–Chiari syndrome (BCS) is defined as hepatic outflow obstruction regardless of the cause or level of obstruction—from small hepatic veins to the opening of the inferior vena cava in the right atrium. BCS could be primary or secondary. Very few cases of this syndrome have been reported in Nigeria and there is no local clinical series documenting the noninvasive and invasive imaging findings and importance of interventional radiology techniques in its diagnosis and management.

We report three cases of patients diagnosed with BCS in Lagos, Nigeria. We hope this work will raise awareness about the condition and its associations and show that much can be done to establish diagnosis and care with minimally invasive techniques in our resource-limited environment.

Keywords

Budd–Chiari syndrome - Nigeria - interventional radiology - transjugular intrahepatic postosystemic stent-shunt - venoplasty

Publikationsverlauf

Artikel online veröffentlicht:
04. Oktober 2021

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