CC BY 4.0 · European J Pediatr Surg Rep. 2022; 10(01): e111-e114
DOI: 10.1055/s-0042-1750134
Case Report

Emergency Separation of Extreme VLBW Omphalopagus Twins: Case Report

Waleed Burhamah
1   Royal College of Surgeons in Ireland, Dublin, Ireland
,
Amar Alnaqi
2   Department of Pediatric Surgery, Ibn Sina Hospital, Sabah Medical Center, Kuwait, Kuwait
,
Yaqoub Jafar
2   Department of Pediatric Surgery, Ibn Sina Hospital, Sabah Medical Center, Kuwait, Kuwait
,
2   Department of Pediatric Surgery, Ibn Sina Hospital, Sabah Medical Center, Kuwait, Kuwait
› Author Affiliations

Abstract

The classification of conjoint twins is based according to the site of attachment. The challenges in management of such anomalies span the entire continuum of care from delivery to resuscitation to separation and finally discharge. Scheduled separation is ideal, occasionally the caring team is faced with no option but to perform an emergent separation. Omphalopagus is a type of conjoined twinning characterized by union of the peritoneal cavities through an infraumbilical abdominal wall defect. In this report we describe our experience with a successful emergency separation of extremely preterm omphalopagus twins.

This is the first case of conjoint twins in Kuwait, we highlight the challenges faced, stressing the importance of adhering to antenatal care as well as management by a multidisciplinary team.



Publication History

Received: 10 December 2021

Accepted: 22 April 2022

Article published online:
04 July 2022

© 2022. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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