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Int J Angiol 2023; 32(04): 207-214
DOI: 10.1055/s-0043-1767759
Review Article

Review of Advances on Management of Chronic Thromboembolic Pulmonary Hypertension

Sanjay Tyagi
1   Department of Cardiology, G B Pant Institute of Postgraduate Medical Education and Research, New Delhi, India
,
Vishal Batra 
1   Department of Cardiology, G B Pant Institute of Postgraduate Medical Education and Research, New Delhi, India
,
Ankur Gautam
1   Department of Cardiology, G B Pant Institute of Postgraduate Medical Education and Research, New Delhi, India
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Abstract

Chronic thromboembolic pulmonary hypertension is rare, underdiagnosed form of pulmonary hypertension. It is caused by intravascular obstruction of pulmonary arteries due to fibrotic transformation of thromboembolic material and microvasculopathy. It is important to diagnose this variant as potentially curative treatment in the form of pulmonary endarterectomy is available. Last two decades have seen rapid advances in targeted medical management and refinement in balloon pulmonary angioplasty technique, which have provided a viable therapeutic option for patients who deemed to be inoperable.

Keywords

chronic thromboembolic pulmonary hypertension - pulmonary embolism - balloon pulmonary angioplasty - ventilation perfusion scan - pulmonary endarterectomy - right heart catheterization - pulmonary artery pressure


Publication History

Article published online:
16 April 2023

© 2023. International College of Angiology. This article is published by Thieme.

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