Craniosynostosis in 2-Month-Old Infant Managed with Minimally Invasive Endoscopically Assisted Remodelation (MEAR)

Abstract

Craniosynostosis is an atypical closure of one or multiple sutures that cause abnormal skull shape. Main complications include intracranial hypertension, alteration of cognitive development, seizures, and blindness, among others. The incidence is 1 in 2000 live births, and it is higher in males. This case report presented a 2-month-old infant with scaphocephaly identified on the physical examination. The early approach was a CT scan and cephalometric assessment to confirm the diagnosis and Schedule the surgery treatment. The minimally invasive endoscopic remodeling was successfully performed with positive outcomes. Literature review was performed on digital bases like PubMed, Web of Science and Scopus. Minimally invasive endoscopically assisted remodelation (MEAR) benefits to correct craniosynostosis are a shorter stay at hospital, less perioperative complications and lower medical cost. Using technologies and innovative techniques the surgical approach could be improved to reduce complications and maximize outcomes. Thus, neurosurgery departments must know and implement this technique.

Resumo

A craniossinostose é um fechamento atípico de uma ou múltiplas suturas que causa formato anormal do crânio. As principais complicações incluem hipertensão intracraniana, alteração do desenvolvimento cognitivo, convulsões e cegueira, entre outras. A incidência é de 1 em 2000 nascidos vivos, sendo maior em homens. Este relato de caso apresentou um bebê de 2 meses com escafocefalia identificada no exame físico. A abordagem inicial foi uma tomografia computadorizada e avaliação cefalométrica para confirmar o diagnóstico e programar o tratamento cirúrgico. A remodelação endoscópica minimamente invasiva foi realizada com sucesso, com resultados positivos. A revisão da literatura foi realizada em bases digitais como PubMed, Web of Science e Scopus. Os benefícios da remodelação assistida endoscópica minimamente invasiva (MEAR) para corrigir a craniossinostose são menos tempo no hospital, menos complicações perioperatórias e menor custo médico. Usando tecnologias e técnicas inovadoras, a abordagem cirúrgica pode ser melhorada para reduzir complicações e maximizar os resultados. Portanto, os departamentos de neurocirurgia devem conhecer e implementar esta técnica.

Keywords

craniosynostosis - minimally invasive - endoscopic - case report

Palavras-chave

craniossinostose - minimamente invasivo - endoscópico - relato de caso

Publikationsverlauf

Eingereicht: 01. Februar 2023

Angenommen: 23. Oktober 2024

Artikel online veröffentlicht:
27. März 2025

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