Zusammenfassung
Ulzerative Kolitis ist eine chronische Entzündung des Kolons, gekennzeichnet durch
zeitweilige Exazerbation und Remission. Es kann durch Darmkrebs oder durch eine autoimmun
bedingte, extraintestinale Manifestation erschwert werden. Wir stellen hier das Krankheitsbild
einer Frau mit ulzerativer Kolitis dar, die die folgenden Krankheiten entwickelte:
Sarkoidose, Darmkrebs, primär sklerosierende Cholangitis (PSC) und Gallengangskarzinom.
Unserem Wissen nach wurden diese Symptome bisher noch nie bei einem Patienten in solch
einer Kombination festgestellt.
Abstract
Ulcerative colitis is a chronic inflammatory disease of the colon characterized by
intermittent exacerbations and remissions. It may be complicated with colon cancer
or autoimmune-related extracolonic problems. Herein, we present a woman with ulcerative
colitis who developed sarcoidosis, colon cancer, primary sclerosing cholangitis, and
cholangiocarcinoma. To our knowledge, such associations in a patient have not been
reported before.
Schlüsselwörter
ulzerative Kolitis - entzündliche Darmerkrankung - primär sklerosierende Cholangitis
- Kolonkrebs - Gallengangkarzinom - malignes Cholangiom - Sarkoidose
Key words
autoimmune disease - ulcerative colitis - inflammatory bowel disease - primary sclerosing
cholangitis - colon cancer - bile duct carcinoma - cholangiocarcinoma - sarcoidosis
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