Objective: Is there more than coincidence of developmental delay, CSWS-like episodes in EEG and
progressive unilateral cerebellar atrophy?
Method: A severly mentally retarded 18 years old boy, with developmental delay from birth,
shows epilepsy with predominantly petit mal seizures and rare grand mal since the
age of 4 to 6 years. The EEG is fluctuating all over the years with CSWS-status like
episodes and multiregional epileptic activity over the parieto-occipital regions.
Additionally there is progressive leftsided cerebellar atrophy.
Results: Until know we have no explanation for this coincidence of developmental delay, CSWS-like
episodes and progressive cerebellar atrophy. Could it be a process similar to Rasmussen
encephalitis? Biopsy was not yet done.
