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DOI: 10.1055/s-2007-1022109
Protein-losing Enteropathy after Fontan Operation for Tricuspid Atresia (Imperforate Tricuspid Valve)
Publication History
1980
Publication Date:
19 March 2008 (online)
Summary
Protein-losing enteropathy occurred in a 7-year-old girl with tricuspid atresia, concordant ventriculo-arterial connexions and a relatively large hypoplastic right ventricle, one year after an atrio-ventricular type of Fontan operation by means of a valveless woven Dacron conduit. Severe conduit regurgitation and a marked enlargement of the hypoplastic right ventricle were demonstrated at recatheterization. Insertion of a bioprosthetic valve at the base of the right atrial appendage led to a dramatic clinical recovery of the patient.
The use of a valved conduit is recommended when an atrioventricular type of Fontan repair is planned in patients with tricuspid atresia, concordant ventriculo-arterial connexions and relatively large hypoplastic right ventricle.
Key words
Protein-losing enteropathy - Fontan operation - Hypoplastic right ventricle - Conduit regurgitation