ABSTRACT
Several renal vascular pathological processes have been associated with hematuria.
These include renal artery aneurysm (RAA), fibromuscular dysplasia (FMD), renal nutcracker
syndrome (RNS), renal arteriovenous malformation, renal vasculitis, and renal artery
or vein thrombosis. We present an unusual case of hematuria in a patient eventually
diagnosed with RAA, FMD, and RNS. Percutaneous therapy, including endovascular coiling,
percutaneous transluminal angioplasty, and stent placement were used to address the
underlying pathology. The differential diagnosis, pathophysiology, and surgical and
interventional management of these renal vascular disorders are reviewed.
KEYWORDS
Hematuria - fibromuscular dysplasia - nutcracker syndrome - renal artery aneurysm
- vasculitis - coil - angioplasty - stent
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Gregory J DubelM.D.
Division of Interventional Radiology, Rhode Island Hospital
593 Eddy Street, 3rd Floor Main Building, Providence, RI 02903