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Neuropediatrics 1991; 22(3): 115-120
DOI: 10.1055/s-2008-1071429
Original article

© Georg Thieme Verlag KG Stuttgart · New York

Neuroradiological Findings in Sturge-Weber Syndrome (SWS) and Isolated Pial Angiomatosis

P.  Terdjman1 , J.  Aicardi2 , C.  Sainte-Rose3 , F.  Brunelle1
  • 1Service de Radiologie (Pr D. Lallemand), Hôpital des Enfants Malades, 149 rue de Sèvres, F-75743 Paris Cedex 15, France
  • 2Unité de Neurologie et INSERM, Hôpital des Enfants Malades, 149 rue de Sèvres, F-75743 Paris Cedex 15, France
  • 3Service de Neurochirurgie (Pr Hirsch), Hôpital des Enfants Malades, 149 rue de Sèvres, F-75743 Paris Cedex 15, France
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Publication History

Publication Date:
19 March 2008 (online)

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Abstract

In 14 children with Sturge-Weber syndrome, cortical calcifications on CT scan was present in 12, localized brain atrophy in 10, enlargement of the choroid plexus in 7, and abnormal veins in 7. Cortical enhancement was present on 12 CTs performed shortly after an episode of severe seizures or hemiplegia but was absent or considerably less marked at a distance from the acute episodes. We suggest that cortical enhancement is related to seizure activity and/or blood-brain disturbances rather than to the extension of pial angioma.

Key words

Sturge-Weber syndrome - Children central nervous system - Brain calcifications - Brain angioma

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