David-V Procedure in a Patient with Aortic Dilation and Competent Quadricuspid Aortic Valve: Are Genetics to Blame?

Katherine R. Hebeler; John J. Squiers; Heike Baumgarten; J. Michael DiMaio; William T. Brinkman

doi:10.12945/j.aorta.2016.16.033

AORTA, Table of Contents

CC BY 4.0 · Aorta (Stamford) 2016; 04(05): 178-180
DOI: 10.12945/j.aorta.2016.16.033

Case Report

Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

David-V Procedure in a Patient with Aortic Dilation and Competent Quadricuspid Aortic Valve: Are Genetics to Blame?

Authors

Katherine R. Hebeler

¹Department of Cardiothoracic Surgery, The Heart Hospital Baylor Plano, Plano, Texas, USA
John J. Squiers

¹Department of Cardiothoracic Surgery, The Heart Hospital Baylor Plano, Plano, Texas, USA
Heike Baumgarten

¹Department of Cardiothoracic Surgery, The Heart Hospital Baylor Plano, Plano, Texas, USA
J. Michael DiMaio

¹Department of Cardiothoracic Surgery, The Heart Hospital Baylor Plano, Plano, Texas, USA
William T. Brinkman

¹Department of Cardiothoracic Surgery, The Heart Hospital Baylor Plano, Plano, Texas, USA

Abstract

Quadricuspid aortic valves (QAVs) are extremely rare. In this case study, we report a David-V valve-sparing aortic root replacement with reimplantation of a native QAV in a patient with aortic dilation, normal valve function, and a family history of aortic dissection. Microscopic pathological examination of the excised section of the aorta revealed scattered small foci of cystic medical degeneration throughout. A genetic predisposition for aortic dilation may be present in patients with QAV, even in the setting of a competent valve. Regular screening for aortic dilation in patients with known QAV should therefore be considered.

Key Words

Quadricuspid aortic valve - Aortic dilation - Genetics

Full Text

References

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