Limb Body Wall Complex: A Rare Anomaly

ABSTRACT

We present autopsy findings of a case of limb body wall complex (LBWC). The fetus had encephalocele, genitourinary agenesis, skeletal anomalies and body wall defects. The rare finding in our case is the occurrence of both cranial and urogenital anomalies. The presence of complex anomalies in this fetus, supports embryonal dysplasia theory of pathogenesis for LBWC.

Key words:

Encephalocele - limb body wall anomaly - skeletal anomalies - urogenital agenesis

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