Necrotizing Sarcoid Granulomatosis is the term given to a variant of Sarcoidosis in
which the granulomas show necrosis and evidence of angitis. This variant of sarcoidosis
tends to involve the lungs primarily; however central nervous system (CNS) involvement
has also been reported. We report here a case of extra-dural cord compression at cranio-vertebral
junction with no other systemic involvement and excellent clinical response to corticosteroids
alone. Recognition of this rare variant of sarcoidosis by the pathologist and prompt
institution of corticosteroids by the clinician will generally give very gratifying
results, as was seen in the present case.
Key words
Cranio-vertebral junction - necrotizing sarcoid granulomatosis - compressive myelopathy
