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CC BY-NC-ND 4.0 · The Arab Journal of Interventional Radiology 2018; 2(02): 64-70
DOI: 10.4103/AJIR.AJIR_23_18
Review Article

Endovascular Treatment of Pulmonary Arteriovenous Malformations: How We Do It

Xin Li
Department of Radiology, University Hospital Cleveland Medical Center, Case Western Reserve University, Cleveland, Ohio, USA
,
Leen Alkukhun
Department of Radiology, University Hospital Cleveland Medical Center, Case Western Reserve University, Cleveland, Ohio, USA
,
Sasan Partovi
Department of Radiology, University Hospital Cleveland Medical Center, Case Western Reserve University, Cleveland, Ohio, USA
,
Victor Kondray
Department of Radiology, University Hospital Cleveland Medical Center, Case Western Reserve University, Cleveland, Ohio, USA
,
Mohammed Al-Natour
Department of Radiology, University Hospital Cleveland Medical Center, Case Western Reserve University, Cleveland, Ohio, USA
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Pulmonary arteriovenous malformation (PAVM) is a rare disease disproportionally affecting patients with hereditary hemorrhagic telangiectasia and may be associated with other pulmonary or infectious etiologies. Respiratory symptoms are the most common, including dyspnea, hypoxemia, and hemoptysis. Due to the impairment of normal pulmonary filtration function, patients with PAVM are at risk for embolic events, ranging from ischemic strokes to brain abscesses. More importantly, PAVM can enlarge over time or with physiological changes, which may lead to catastrophic hemorrhages and increased embolization risks. From imaging perspective, echocardiography with contrast bubbles and computed tomography can both be used to diagnose PAVMs with high sensitivity and specificity. Treatment modalities have evolved from invasive surgeries to transluminal catheter-based interventions. In recent decades, the evolution of interventional techniques and equipment has resulted in a high technical success rate for the treatment of PAVMs. Here, we present the interventional PAVM treatment protocol at our institution.

Interventional treatment - multidetector computed tomography - pulmonary arteriovenous malformation - transthoracic contrast echocardiography


Publication History

Article published online:
10 April 2021

© 2018. The Arab Journal of Interventional Radiology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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