Malignant Peripheral Nerve Sheath Tumor of the Pelvic Retroperitoneum Misdiagnosed as Carcinoma Ovary

Murali Subbaiah; Bhawna A Badhe; Gowri Dorairajan; Priyadarshini Dehuri

doi:10.4103/ijmpo.ijmpo_47_17

Indian Journal of Medical and Paediatric Oncology, Table of Contents

CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2018; 39(02): 234-236
DOI: 10.4103/ijmpo.ijmpo_47_17

Practitioner Section

Malignant Peripheral Nerve Sheath Tumor of the Pelvic Retroperitoneum Misdiagnosed as Carcinoma Ovary

Authors

Murali Subbaiah

Department of Obstetrics and Gynaecology, JIPMER, Puducherry, India
Bhawna A Badhe

Department of Pathology, JIPMER, Puducherry, India
Gowri Dorairajan

Department of Obstetrics and Gynaecology, JIPMER, Puducherry, India
Priyadarshini Dehuri

Department of Pathology, JIPMER, Puducherry, India

Abstract

A 52-year-old postmenopausal female was found to have a large solid cystic adnexal mass, compressing the right ureter, and was suspected to have carcinoma ovary. However, it turned out to be a retroperitoneal neurogenic tumor. Malignant peripheral nerve sheath tumors (MPNST) may have cystic areas and may be misdiagnosed as ovarian tumors. Treatment of MPNST involves complete surgical excision of the tumor with a wide margin.

Keywords

Malignant peripheral nerve sheath tumor - neurogenic tumor - retroperitoneal tumor

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References

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