Prenatally diagnosed case of tricuspid valve dysplasia: A case report with review of the literature

Prateek Agarwal; Rajesh Agarwal

doi:10.4103/ijri.IJRI_463_18

Indian Journal of Radiology and Imaging, Table of Contents

CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2019; 29(04): 452-456
DOI: 10.4103/ijri.IJRI_463_18

Case Report

Prenatally diagnosed case of tricuspid valve dysplasia: A case report with review of the literature

Prateek Agarwal

Department of Radiodiagnosis, Kempegowda Institute of Medical Sciences, Bengaluru, Karnataka

,

Rajesh Agarwal

Department of Ultrasound, Meera Hospital, Shiv Marg, Bani Park, Jaipur, Rajasthan, India

› Author Affiliations

Abstract

We present a case of fetal tricuspid valve dysplasia (TVD) and pulmonary atresia, diagnosed during a routine obstetric ultrasound scan. Serial fetal echocardiographic evaluations revealed progressively augmented prodigious thickening of the tricuspid valvular and subvalvular structures, which eventually extensively obliterated the right ventricle cavity. Thickened dysplastic valve displayed a “cotton-wool” appearance. Unusual configurations of three vessels in the three-vessel view were also observed on a consecutive gray scale and color Doppler scans. During pregnancy, the fetus exhibited satisfactory growth parameters, and complications of progressive hemodynamic compromise associated with TVD and pulmonary atresia such as grievous hydrops or arrhythmia did not develop till 39 weeks of gravidity.

Keywords

Dysplasia - non-immune hydrops - pulmonary atresia - tricuspid annulus - tricuspid regurgitation - tricuspid valve

Full Text

References

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