Introduction:
Sarcoidosis a chronic, idiopathic, multisystemic disease of unknown etiology with
frequent pulmonary and lymphatic systemic manifestations (90%). Manifestations in
the head and neck are occuring in 10% of the patients with Sarcoidosis.
Methods:
case report: A 40 year old male adult is presenting a progressive hearing loss since
a couple of years as well as a mild pressure felling over the mastoid. Two years before
he had surgery of the right nasolacrimal duct.
Results:
The clinical examination of the tympanic membran and the ear by microscope was regulary
and without any pathology. Audiometrically we see a sensoneurial hearing loss of 1
KHz by 40 dB up to 4 KHz by 60 dB. MR shows a chronic mastoititis as well as a meningitis.
The labyrinth was without any pathology. In the OR mastoidectomy was performed. Frozen
section showed a granulomatous inflammation. After fixation the diagnosis of the sarcoidosis
were proposed.
Conclusions:
This is a rare case of a extrapulmonary sarcoidosis in the mastoid. A CT of the thorax
showed a sarcoidosis stage I with bihilare lymphatic manifestation. The patient responded
to the treatment with Soludecortin of 50 mg/d. The hearing loss is still persisting.