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Neuropediatrics 2013; 44(03): 171-173
DOI: 10.1055/s-0032-1329908
Short Communication
Georg Thieme Verlag KG Stuttgart · New York

Isolated Intraspinal Juvenile Xanthogranuloma in an Infant Presenting as Acute Paraplegia

David-Alexander Wille
1   Department of Neuropediatrics, University Children's Hospital Zurich, Zurich, Switzerland
,
Oliver Bozinov
2   Department of Neurosurgery, University Hospital Zurich, Zurich, Switzerland
,
Ianina Scheer
3   Department of Neuroradiology, University Children's Hospital Zurich, Zurich, Switzerland
,
Michael A. Grotzer
4   Department of Oncology, University Children's Hospital Zurich, Zurich, Switzerland
,
Eugen Boltshauser
1   Department of Neuropediatrics, University Children's Hospital Zurich, Zurich, Switzerland
› Author Affiliations
Further Information

Publication History

25 June 2012

01 October 2012

Publication Date:
19 December 2012 (online)

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Abstract

Juvenile xanthogranuloma is a histiocytic proliferative disease that predominantly affects the skin. Extracutaneous involvement is rare. We present the case of a 6-month-old infant with acute paraplegia. Magnetic resonance imaging showed an intraspinal extradural mass at midthoracic level with marked compression of the spinal cord. Complete tumor removal was achieved by emergency surgery and was followed by complete neurologic recovery. Histologic examination led to the diagnosis of a juvenile xanthogranuloma. To the best of our knowledge, an isolated intraspinal juvenile xanthogranuloma in the first 12 months of life has not been described before.

Keywords

juvenile xanthogranuloma - children - paraplegia - spinal cord
 

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