Das Parsonage-Turner-Syndrom

Zusammenfassung

Die neuralgische Schultermyatrophie (Parsonage-Turner-Syndrom) ist eine selten auftretende, akute periphere Neuropathie des Plexus cervicobrachialis. Die genaue Ursache der Erkrankung ist nicht bekannt. Die Diagnose kann aufgrund der Anamnese und körperlichen Untersuchung gestellt werden. Ergänzend ist die Durchführung einer Magnetresonanztomografie (MRT) der betroffenen Schulter und ggf. der HWS zum Ausschluss konkurrierender Ursachen sinnvoll. Eine spezifische Therapie existiert nicht. Die Erkrankung heilt in Abhängigkeit von der Intensität der Erstmanifestation in etwa 50 – 67% der Fälle innerhalb von 2 bis 3 Jahren aus. Bei unvollständiger Erholung können neurologische Defizite verbleiben, insbesondere nach wiederholten Attacken an derselben Extremität.

Abstract

Neuralgic amyotrophy of the shoulder (Parsonage-Turner syndrome) is a rare condition of unknown aetiology which manifests as acute neuropathy of the brachial plexus. Diagnosis is based on typical symptoms and physical examination. In addition, magnetic resonance imaging of the affected shoulder and the cervical spine is advisable, in order to distinguish this syndrome from other conditions with similar symptoms. There is no specific treatment for neuralgic amyotrophy, but in about 50 – 67% of cases complete recovery occurs within two to three years, depending on the severity of the symptoms when they first appear. In patients whose strength and function are not fully restored, neurological deficits may remain, especially if the same shoulder is affected by recurrent attacks.

Schlüsselwörter

Parsonage-Turner-Syndrom - neuralgische Schultermyatrophie - akute Neuropathie des Plexus cervicobrachialis

Key words

Parsonage-Turner syndrome - neuralgic amyotrophy of the shoulder - acute neuropathy of the brachial plexus

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