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Neuropediatrics 1980; 11(1): 72-75
DOI: 10.1055/s-2008-1071376
Case reports

© Georg Thieme Verlag KG Stuttgart · New York

THE "STARTLE DISEASE" IN BRAIN-DAMAGED PATIENTS: REPORT OF A CASE

W. K. Baier
  • Dept. of Neuropediatrics, University of Kiel, F.R.G.
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Publication History

Publication Date:
19 March 2008 (online)

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Abstract

It is reported about one case of so-called startle disease in brain-damaged patients in a 7 year-old girl. Furthermore, two related, non-epileptic paroxysmal startle syndromes, the "essential startle disease" and the "hereditary startle syndrome" are described and constrasted with "epileptic seizures induced by unexpected sensory stimuli" or "startle epilepsy". The overt participation of conditioning factors in the present case is understood as a hint at a possible therapeutic access.

Key words

Startle disease - startle epilepsy - hyperexplexia

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