Connexin30 (Gjb6)-deficiency causes severe hearing impairment and lack of endocochlear potential. - Teubner,B.; Michel,V.; Pesch,J.; Lautermann,J.; Cohen-Salmon,M.; Sohl,G.; Jahnke,K.; Winterhager,E.; Herberhold,C.; Hardelin,J.P.; Petit,C.; Willecke,K. (Hum Mol Genet, 2003)