Subunit composition of plasma von Willebrand factor. Cleavage is present in normal individuals, increased in IIA and IIB von Willebrand disease, but minimal in variants with aberrant structure of individual oligomers (Types IIC, IID and IIE) - Zimmerman, TS; Dent, JA; Ruggeri, ZM (J Clin Invest, 1986)
et al.