Surgical Reconstruction after Resection of a Large Myxofibrosarcoma of the Upper Extremity^[*]

Abstract

Myxofibrosarcoma is a rare soft tissue sarcoma. The authors present a case report regarding the excision and reconstruction of an extensive low-grade myxofibrosarcoma in the forearm, in the wrist, and in the hand of a young woman. A large-scale monobloc excision was performed according to resonance magnetic imaging (MRI) and transoperative histopathologic study findings. A dermal matrix and total skin graft associated with a postoperative physiotherapy program were used. The aspects related to the differential diagnosis of myxofibrosarcoma in a young patient, its infiltrative character, the extensive excision, the reconstruction in two surgical times (using a dermal matrix and a full-thickness skin graft), and the postoperative physical therapy program were considered important.

Keywords

sarcoma - soft tissue neoplasms - rehabilitation

^* Work developed at the Rede Sarah de Hospitais de Reabilitação, Brasília, DF, Brazil.

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