Abstract
Soft-tissue tumors are rare in the pediatric population. First described in 1969 as
myxoma of the nerve sheath, the neurothekeoma is a benign tumor lesion with presumable
origin in the nerve sheath. It occurs mainly in female children and presents as a
mass of slow, subcutaneous growth, asymptomatic and without alteration of the local
pigmentation. It is predominantly located in the head, neck, and extremities of the
upper limbs. This report presents the case of a 16-year-old male with a tumor mass
originating from the nerve sheath in the 4th left metacarpal, intraosseous, and relapsed after previous surgical resection 2 years
before this observation. A marginal resection of the tumor mass was performed on the
distal region of the fourth metacarpal, followed by curettage of the proximal phalanx
and filling with structural autologous bone graft. The patient maintained a favorable
postoperative clinical evolution, without local pain or range of motion limitation
in his fingers. Radiologically, a progressive trabecular filling of the proximal phalanx
of the fourth metacarpal was observed. At 17 months of follow-up, the patient is asymptomatic
and shows no signs of relapse. The description of this case serves to increase the
familiarity with this rare pathology, and aid its diagnosis and treatment.
Keywords
neurothekeoma - hand - soft tissue neoplasms - biopsy
