CC BY-NC-ND 4.0 · Rev Bras Ortop (Sao Paulo) 2020; 55(05): 649-652
DOI: 10.1016/j.rboe.2017.10.010
Relato de Caso
Ortopedia Pediátrica

Spondylectomy for Primary Ewing Lumbar Sarcoma in Children[*]

Article in several languages: português | English
1   Department of Orthopedic Surgery, Unidade Local de Saúde do Alto Minho, Viana do Castelo, Portugal
,
Luísa Vital
2   Department of Orthopedic Surgery, Hospital de São João, Faculdade de Medicina, Universidade do Porto, Porto, Porto, Portugal
,
Francisco Serdoura
2   Department of Orthopedic Surgery, Hospital de São João, Faculdade de Medicina, Universidade do Porto, Porto, Porto, Portugal
,
André Rodrigues Pinho
2   Department of Orthopedic Surgery, Hospital de São João, Faculdade de Medicina, Universidade do Porto, Porto, Porto, Portugal
,
Vitorino Veludo
2   Department of Orthopedic Surgery, Hospital de São João, Faculdade de Medicina, Universidade do Porto, Porto, Porto, Portugal
› Author Affiliations

Abstract

Primary Ewing sarcoma in the spine is very rare, and the treatment for it is multidisciplinary. There is no consensus regarding the optimal method of local control; however, en bloc resection is associated with an improvement in survival rates. The authors report a case of a 5-year-old girl who initially presented low back pain, and was diagnosed with Ewing sarcoma after being submitted to imaging studies by radiography, magnetic resonance and bone biopsy. A spondylectomy was performed in accordance with the Euro Ewing protocol. At the three-year follow-up, the patient had no restrictions regarding her daily activities, and there has been no evidence of recurrence to date.

* Study conducted at the Department of Orthopedic Surgery, Hospital de São João, Faculsade de Medicina, Universidade do Porto, Porto, Portugal. Originally Published by Elsevier.




Publication History

Received: 06 September 2017

Accepted: 19 October 2017

Article published online:
03 February 2020

© 2020. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

Sociedade Brasileira de Ortopedia e Traumatologia. Published by Thieme Revinter Publicações Ltda
Rio de Janeiro, Brazil

 
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