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DOI: 10.1055/a-2698-3658
Surgical Repair of Ectopia Cordis in a Sub-Saharan African Country (Benin)
Authors

Abstract
Background
Ectopia cordis (EC) is an exceptionally rare congenital anomaly with a poor prognosis, particularly in resource-limited settings.
Case Description
We present a newborn with complete thoracic EC who underwent surgical correction on day 5 of life. Although cardiac repositioning and soft tissue coverage were achieved, the infant died 72 hours postoperatively from septic shock, reflecting the significant challenges faced in such contexts.
Conclusion
This case underscores the urgent need for improved antenatal care and technical resources to enhance outcomes for complex congenital anomalies in sub-Saharan Africa.
Patients' Consent
Written informed consent was obtained from the patient's legal guardians for publication of this case and associated images.
Publikationsverlauf
Eingereicht: 27. April 2025
Angenommen: 09. September 2025
Accepted Manuscript online:
10. September 2025
Artikel online veröffentlicht:
18. September 2025
© 2025. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)
Georg Thieme Verlag KG
Oswald-Hesse-Straße 50, 70469 Stuttgart, Germany
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References
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