Interhemispheric–Transcortical Approach for Resection of an Atypical Teratoid/Rhabdoid Tumor (AT/RT) of the Left Lateral and Third Ventricle

Abstract

Introduction

Atypical teratoid/rhabdoid tumors (AT/RT) are malignant central nervous system (CNS) tumors that represent 3% of all pediatric CNS tumors. Majority of cases have SMARCB1 gene mutations and historically carried a poor prognosis.

Case Presentation

A 9-year-old boy was diagnosed with a third ventricle AT/RT and initially underwent endoscopic surgical biopsy. Subsequent tumor resection was completed using an interhemispheric–transcortical approach.

Lessons

Surgical approaches to ventricular system must be tailored to the tumor characteristics on a case-by-case basis. We present a case using a transcortical approach for understanding of the microsurgical anatomy for safe resection of a third ventricle AT/RT.

Keywords

AT/RT - atypical teratoid/rhabdoid tumor - ventricular surgery - pediatric neuro-oncology - high-grade glioma

Publikationsverlauf

Eingereicht: 18. Juni 2025

Angenommen: 24. Juni 2025

Artikel online veröffentlicht:
30. September 2025

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