Atypical Chordoid Glioma of the Third Ventricle: A Case Report

Abstract

Chordoid glioma of the third ventricle was classified as a rare tumor by the World Health Organization in 2000. Approximately 55 cases have been reported so far in world literature. These tumors are usually slow growing presenting with features of raised ICP. Most tumors have low proliferative index and these tumors are immunohistochemically negative for P⁵³. We are reporting a case of chordoid glioma of the third ventricle, with atypical features of high proliferative index and P⁵³ positivity on immunohistochemistry.

Keywords

chordoid glioma - KI-67 - P⁵³ - third ventricle - immunohistochemistry (IHC)

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