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CC BY-NC-ND 4.0 · Thorac Cardiovasc Surg Rep 2017; 06(01): e10-e14
DOI: 10.1055/s-0037-1598625
Case Report: Thoracic
Georg Thieme Verlag KG Stuttgart · New York

It's Rare So Be Aware: Pleuropulmonary Blastoma Mimicking Congenital Pulmonary Airway Malformation

Fayza Haider
1   Pediatric Surgery Unit, Department of Surgery, Salmaniya Medical Complex, Manama, Bahrain
,
Khulood Al Saad
2   Pediatric Department, Salmaniya Medical Complex, Manama, Bahrain
,
Fatima Al-Hashimi
3   Department of Pathology, Salmaniya Medical Complex, Manama, Bahrain
,
Hakima Al-Hashimi
4   Department of Radiology, Salmaniya Medical Complex, Manama, Bahrain
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Weitere Informationen

Publikationsverlauf

30. Oktober 2016

10. Januar 2017

Publikationsdatum:
11. April 2017 (online)

   Lizenzen und Reprints

Abstract

Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood. The tumor arises in the lung and pleura and is regarded as a pulmonary dysontogenetic or embryonic neoplasm. Four types are defined in literature. Type I PPB is a rare, cystic lung neoplasm in infants characterized by subtle malignant changes and a good prognosis. Recurrences after type I PPB are usually advanced with a poor prognosis.

We report this case to increase awareness about this entity so that the pediatricians, pediatric surgeons, radiologist, and pathologist recognize it early.

Keywords

Pleuropulmonary Blastoma - lung - benign or congenital lesions - airway (includes related subject matter) - infant - pediatric
 

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