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Thorac Cardiovasc Surg 2017; 65(08): 639-648
DOI: 10.1055/s-0037-1604469
Review Article
Georg Thieme Verlag KG Stuttgart · New York

Surgical Treatment of Ebstein's Anomaly

Melchior Burri
1   Clinic for Cardiovascular Surgery, German Heart Centre Munich at the Technical University, Munich, Germany
,
Rüdiger Lange
1   Clinic for Cardiovascular Surgery, German Heart Centre Munich at the Technical University, Munich, Germany
2   DZHK (German Centre for Cardiovascular Research), Partner Site Munich Heart Alliance, Munich, Germany
› Author Affiliations
Further Information

Publication History

30 March 2017

13 June 2017

Publication Date:
14 August 2017 (online)

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Abstract

Surgical repair of the tricuspid valve is a milestone in the medical history of patients with Ebstein's anomaly. The timely alleviation of the insufficiency has an important impact on the prognosis. In this review, we describe features of the disease relevant to surgical correction and the evolution of surgical techniques over six decades. We compare the results of different repair and replacement techniques. Additionally, we discuss concomitant antiarrhythmic surgery and bailout strategies for postoperative right ventricular failure. Finally, we review the surgical options in symptomatic neonates with Ebstein's disease.

Keywords

heart valve surgery - congenital heart disease - CHD - tricuspid valve
 

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