CC BY-NC-ND 4.0 · Laryngorhinootologie 2018; 97(S 02): S149-S150
DOI: 10.1055/s-0038-1640228
Otologie: Otology
Georg Thieme Verlag KG Stuttgart · New York

Speech recognition in Patients with Semicircular canals aplasia after Cochlear implantation

A Ahmed
1  Medizinsche Hochschule Hannover-HNO Klinik, Hannover
A Lesinski-Schiedat
2  Medizinsche Hochschule Hannover, Hannover
A Giourgas
2  Medizinsche Hochschule Hannover, Hannover
A Giesemann
2  Medizinsche Hochschule Hannover, Hannover
T Lenarz
2  Medizinsche Hochschule Hannover, Hannover
› Author Affiliations
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Publication History

Publication Date:
18 April 2018 (online)



Cochlea Implants (CI) have become a therapeutic standard for hearing impairment due to the marked improvement in hearing acuity in the vast majority of patients, even in the presence of background noises. In light of the current advances CI is now readily available for patients suffering from inner-ear Dysplasias. However, optimal speech recognition might be restricted. In this retrospective study, we have reviewd all patients in Hannover medical school with Semicircular canals Aplasia (SCA) who have received CI.


22 patients with SCA who successfully received CI had been reviewed retrospectively. 89% of the 22 Patients have CHARGE syndrome (CS) and hence a mental disability in their clinical history. All the preoperative and postoperative radiological imaging as well as audiological data was reviewed. The various speech tests were evaluated according to CAP scale.


The vast majority of patients were successfully with a straight electrode (Nucleus straight electrode) Implanted. All patients developed Hearing ability in classes 1 – 6 according to CAP scale. The Performance could not be explained neither according to the anatomical variation of the cochlea nor by the relative position of the Electrode in relation to the potential position of the cochlear nerve. A broad diversification of the results had been noted.


Basically, CI is recommended in patients with CS and SCA. Acoustic perception alone represents a considerable alleviation in the progression of cognitive therapy. Further investigations should be made in order to be able to make a reliable statement about the cognitive performance in patients with developmental and cognitive delay and the outcome with CI, and if this by itself is an unfavorable prognostic factor.