Schwannoma plexiforme en eminencia tenar

Resumen

El schwannoma plexiforme es un tumor raro, que suele aparecer en tronco, cabeza y cuello. Su diagnóstico definitivo es anatomopatológico, siendo de especial relevancia su distinción con el neurofibroma plexiforme. No se ha descrito potencial de malignización y el tratamiento de elección es la extirpación quirúrgica. Presentamos el caso de un varón de 34 con una tumoración dolorosa en eminencia tenar derecha. Tras realizar RNM que sugiere hemangioma cavernoso, se interviene quirúrgicamente realizándose escisión de la tumoración, cuyo estudio histológico diagnostica de schwannoma plexiforme. A los 12 meses de la cirugía, el paciente se encuentra asíntomático, sin mostrar signos de recidiva o enfermedades asociadas.

Abstract

Plexiform schwannoma is a rare condition that usually presents in the subcutaneous tissue of trunk, head and neck. The definitive diagnosis is based on anatomopathological findings, being plexiform neurofibroma its main differential diagnosis. Malignant transformation of these tumors has not been previously described and surgical excision is the treatment of choice. A case of a 34-year-old male with a painful mass in the thenar eminence of his right hand is presented. MRI suggested cavernous hemangioma and surgical removal of the tumor was performed. Histological analysis confirmed the diagnosis of plexiform schwannoma. At eleven months follow up, the patient was asymptomatic, showing no signs of recurrence or associated diseases.

Palabras Clave

schwannoma - plexiforme - mano

Keywords

schwannoma - plexiform - hand

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