Abstract
Pentalogy of Cantrell (PC) is an uncommon congenital disorder characterized by severe
defects in the chest and abdomen, including abdominal visceral prolapsed via umbilical
cord (omphalocele), defect in the lower part of the sternum, defect in the front of
the diaphragm, defects in the anterior part of the pericardium, and the ectopiacordis.
Here, we report a 2-hour-old girl, weighing 3,500 g, who was referred to Shahid Madani
Hospital in Khorramabad due to the large omphalocele on her chest with pulsating mass
above it. The baby was the first child of a 24-year-old mother who was born with an
uncomplicated vaginal delivery. Very rare cases of PC are born as a term new-born.
Keywords
Pentalogy of Cantrell - omphalocele - pulsatile mass
