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CC BY 4.0 · Aorta (Stamford) 2019; 07(04): 125-128
DOI: 10.1055/s-0039-1693986
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

A Large Ascending Aortic Aneurysm Secondary to Idiopathic Necrotizing Aortitis—A Rare but Important Cause of Thoracic Aortic Disease

Benjamin Smeeton
1   Department of Plastic & Reconstructive Surgery, St. George’s NHS Foundation Trust, London, United Kingdom
,
Muslim Mustaev 
2   Department of Cardiac Surgery, Guys' and St Thomas' NHS Foundation Trust, London, United Kingdom
,
Michael Sabetai
2   Department of Cardiac Surgery, Guys' and St Thomas' NHS Foundation Trust, London, United Kingdom
› Author Affiliations Funding None.
Further Information

Publication History

01 May 2018

09 May 2019

Publication Date:
22 November 2019 (online)

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Abstract

Idiopathic necrotizing aortitis is characterized by lymphoplasmacytic or giant cell-associated inflammation of the aorta, with no specific identifiable cause. We present the case of a 79-year-old man who sought medical attention from his primary care physician because of worsening shortness of breath. The patient underwent an elective ascending aorta, hemiarch, and aortic valve replacement. Histological examination of the aortic specimen demonstrated an unusually thin aorta with features consistent with necrotizing aortitis with giant cell infiltration.

Keywords

idiopathic necrotizing aortitis - aortic aneurysms - ascending aorta hemiarch replacement surgery - aortic valve replacement surgery
 

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