CC BY-NC-ND 4.0 · Journal of Clinical Interventional Radiology ISVIR 2019; 03(03): 189-192
DOI: 10.1055/s-0039-3401352
Case Report
by Indian Society of Vascular and Interventional Radiology

Segmental Arterial Mediolysis with Supra-Aortic Vascular Involvement: Report of Two Cases

1   Department of Radiology, N.M. Virani Wockhardt Hospital, Rajkot, Gujarat, India
› Author Affiliations
Funding No source of support in the form of grants, equipment, drugs, or all of these.
Further Information

Publication History

received 27 May 2019

accepted after revision 01 July 2019

Publication Date:
02 December 2019 (online)

Abstract

Segmental arterial mediolysis (SAM) is a rare noninflammatory vasculopathy predominantly involving the visceral arteries of the abdomen. The most common presentation described is massive intra-abdominal hemorrhage secondary to aneurysm rupture. In this report, we describe two cases with characteristic findings of aneurysm, dissection, and beading involving the visceral arteries and the supra-aortic vessels. SAM involving the supra-aortic vessels is extremely rare.

 
  • References

  • 1 Slavin RE, Gonzalez-Vitale JC. Segmental mediolytic arteritis: a clinical pathologic study. Lab Invest 1976; 35 (01) 23-29
  • 2 Slavin RE, Cafferty L, Cartwright J Jr. Segmental mediolytic arteritis. a clinicopathologic and ultrastructural study of two cases. Am J Surg Pathol 1989; 13 (07) 558-568
  • 3 Slavin RE. Segmental arterial mediolysis: course, sequelae, prognosis, and pathologic-radiologic correlation. Cardiovasc Pathol 2009; 18 (06) 352-360
  • 4 Michael M, Widmer U, Wildermuth S, Barghorn A, Duewell S, Pfammatter T. Segmental arterial mediolysis: CTA findings at presentation and follow-up. AJR Am J Roentgenol 2006; 187 (06) 1463-1469
  • 5 Pillai AK, Iqbal SI, Liu RW, Rachamreddy N, Kalva SP. Segmental arterial mediolysis. Cardiovasc Intervent Radiol 2014; 37 (03) 604-612
  • 6 Tameo MN, Dougherty MJ, Calligaro KD. Spontaneous dissection with rupture of the superior mesenteric artery from segmental arterial mediolysis. J Vasc Surg 2011; 53 (04) 1107-1112
  • 7 Kalva SP, Somarouthu B, Jaff MR, Wicky S. Segmental arterial mediolysis: clinical and imaging features at presentation and during follow-up. J Vasc Interv Radiol 2011; 22 (10) 1380-1387
  • 8 Chao CP. Segmental arterial mediolysis. Semin Intervent Radiol 2009; 26 (03) 224-232
  • 9 Alhalabi K, Menias C, Hines R, Mamoun I, Naidu S. Imaging and clinical findings in segmental arterial mediolysis (SAM).. Abdom Radiol (NY) 2017; 42 (02) 602-611
  • 10 Leu HJ. Cerebrovascular accidents resulting from segmental mediolytic arteriopathy of the cerebral arteries in young adults. Cardiovasc Surg 1994; 2 (03) 350-353
  • 11 Basso MC, Flores PC, de Azevedo Marques A. et al. Bilateral extensive cerebral infarction and mesenteric ischemia associated with segmental arterial mediolysis in two young women. Pathol Int 2005; 55 (10) 632-638
  • 12 Baker-LePain JC, Stone DH, Mattis AN, Nakamura MC, Fye KH. Clinical diagnosis of segmental arterial mediolysis: differentiation from vasculitis and other mimics. Arthritis Care Res (Hoboken) 2010; 62 (11) 1655-1660
  • 13 Lie JT. Segmental mediolytic arteritis. Not an arteritis but a variant of arterial fibromuscular dysplasia. Arch Pathol Lab Med 1992; 116 (03) 238-241
  • 14 Begelman SM, Olin JW. Fibromuscular dysplasia. Curr Opin Rheumatol 2000; 12 (01) 41-47